Übersichtsarbeit

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Morbus Behçet – ein Update

Behçet's disease – an update

Keywords | Summary | Correspondence | Literature


Keywords

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Schlüsselworte

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Summary

Behçet's disease is a systemic vasculitis of unknown etiology, documented in 1937 by the Turkish dermatologist Hulusi Behçet, although the first description of the disease can be found in Volume III of Hippocrates. It is an old disease that continues to raise questions regarding pathogenesis, diagnostic criteria, and treatment algorithm. It is more common described in adults, although first symptoms can appear in adolescence. The aim of the article is an update of this very complicated systemic disease.

Zusammenfassung

Der Morbus Behçet ist eine systemische Vaskulitis unbekannter Ätiologie, die 1937 durch den türkischen Dermatologen Hulusi Behçet beschrieben wurde. Allerdings findet sich die Erstbeschreibung bereits im Band III von Hippocrates. Es handelt sich somit um eine lange bekannte Erkrankung, die auch heute noch Fragen bezüglich ihrer Pathogenese, diagnostischen Kriterien und Behandlungs-Algorithmen aufwirft. Sie tritt häufiger im Erwachsenenalter auf, doch erste Symptome können schon in der Adoleszenz vorkommen. Diese Übersicht der komplexen Erkrankung soll eine aktuelle Bestandsaufnahme liefern.


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Korrespondenz-Adresse

Prof. Dr. Anca Chiriac
Nicolina Medical Center
Dept. of Dermatology
Șoseaua Nicolina, nr. 171 A
RO-700714 Iasi
Email: ancachiriac@yahoo.com

Conflict of Interests

Funding: There was no funding. Conflict of interest statement: The authors declare no conflict of interest. Ethical approvement: The study has been approved by the ethical committee of the Apollonia University, Iasi, Romania

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